|
KMID : 0353420190430040361
|
|
Oral Biology Research
2019 Volume.43 No. 4 p.361 ~ p.364
|
|
|
Intranasal teeth in a 3-year-old child with Smith-Lemli-Opitz syndrome
|
|
Shim Su-Hyun
|
|
|
Abstract
|
|
|
|
Smith?Lemli?Opitz syndrome (SLOS) is a rare autosomal recessive genetic disorder accompanied with congenital anomalies and mental impairment. Clefts of the hard and/or soft palate, small tongue, broad alveolar ridges, and micrognathia have been reported frequently. However, intranasal teeth associated with SLOS have never been described. Here, a case of intranasal teeth in a 3-year-old boy, who was treated operatively for a cleft lip and alveolus at 7 months of age, is reported. Two intranasal teeth were asymptomatic. The teeth were extracted under local anesthesia when they were found to be very loosely attached to the nasal mucosa. Unusual features of this case are highlighted.
|
|
|
KEYWORD
|
|
|
Cleft palate, Smith?Lemli?Opitz syndrome
|
|
|
FullTexts / Linksout information
|
|
|
|
|
Listed journal information
|
|
|